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Document Details :

Title: Primary pulmonary artery rhabdomyosarcoma
Author(s): D. Si , B. Zhang , X. Zhang , M. Zhang , L. Ni , P. Yang
Journal: Acta Cardiologica
Volume: 66    Issue: 3   Date: 2011   
Pages: 391-394
DOI: 10.2143/AC.66.3.2114144

Abstract :
A 69-year-old woman presented with a 4-month history of dyspnoea and radiating upper-right quadrant pain and oedema in her lower extremities for more than 20 days. The ultrasonographic study of the heart revealed the adherence of a substantive hypoechoic mass (73 × 34 mm) to the antelateral wall of the pulmonary artery and resultant pulmonary stenosis. Computed tomographic imaging of the pulmonary artery revealed an irregularly shaped filling defect (approximately 41 × 39 × 59 mm) in the main pulmonary artery. The boundary of the defect was irregular, but demarcation with healthy tissue was clear. After surgical treatment, the histologic and immunohistochemical assays revealed a primary pulmonary artery rhabdomyosarcoma.
Pulmonary artery rhabdomyosarcomas are usually misdiagnosed as other pulmonary artery obstructive diseases. There should be a greater focus of clinical attention and resection is the appropriate surgical treatment for such malignant tumours.