PEETERS ONLINE JOURNALS
Peeters Online Bibliographies
Peeters Publishers
this issue
  previous article in this issuenext article in this issue  

Document Details :

Title: Congenitale gynaecologische malformaties: behandeling
Author(s): GRAUWEN N, HOSTE G, VERGUTS J, DE BRUYNE F
Journal: Tijdschrift voor Geneeskunde
Volume: 70    Issue: 4   Date: 2014   
Pages: 211-218
DOI: 10.2143/TVG.70.04.2001560

Abstract :
Op gynaecologisch vlak bestaan er verschillende soorten congenitale malformaties, elk met hun eigen behandelingsmogelijkheden. De minst voorkomende, maar niet te onderschatten malformatie is vaginale agenese, met als voornaamste oorzaak het syndroom van Mayer-Rokitansky-Küster-­Hauser (MRKH). De behandelingsmogelijkheden bestaan uit het creëren van een neovagina via zelfdilatatie of chirurgie. De meest gekende chirurgische techniek hiervoor is de Vecchietti-methode.






Congenital gynecological malformations
Generally, up to 7% of the population has a congenital gynecological malformation. There are different types of congenital malformations, each with their own complications and therapeutic options.
The least frequent form is vaginal agenesis, mostly part of the Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome. It is characterized by congenital aplasia of the uterus and the upper part of the vagina in women revealing a normal development of the secondary sexual characteristics and a normal 46 XX karyotype. The creation of a neovagina by dilatation techniques or surgery in these women remains consequential for the psychological and physical aspects of sexual functioning. The best known surgical technique is the Vecchietti procedure. A short description of the MRKH syndrome and the treatment options are presented.


download article




3.85.10.62.