 previous article in this issue | next article in this issue  |
|
Document Details : Title: Electrophysiological findings in Fabry cardiomyopathy: mapping the maze of risk stratification Author(s): J. Li , A. Warth , P. Schnabel , P.A. Schweizer , S.J. Buss , H. Steen , R. Becker , H.A. Katus , D. Thomas Journal: Acta Cardiologica Volume: 67 Issue: 4 Date: 2012 Pages: 481-485 DOI: 10.2143/AC.67.4.2170694 Abstract : We report a case of Anderson-Fabry disease in a young man presenting with cardiac hypertrophy and asymptomatic non-sustained ventricular tachycardia. The patient was referred for evaluation of implantable cardioverter/defibrillator therapy. Assessment of left ventricular ejection fraction is considered the gold standard for identifying patients at risk of sudden cardiac death. However, this patient’s left ventricular function was preserved. Electrophysiological study did not reveal inducible arrhythmia or cardiac conduction abnormalities. Review of the literature indicates limited knowledge on the electrophysiology of Fabry cardiomyopathy and highlights the need for optimized risk stratification strategies. |
