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Document Details : Title: Light chain deposition disease as a rare cause of restrictive cardiomyopathy Author(s): P. Koopman , J. Van Dorpe , B. Maes , K. Dujardin Journal: Acta Cardiologica Volume: 64 Issue: 6 Date: 2009 Pages: 821-824 DOI: 10.2143/AC.64.6.2044752 Abstract : We report an unusual case of a 47-year-old Caucasian woman who presented with severe dyspnoea as a manifestation of restrictive cardiomyopathy, found to be due to myocardial deposition of kappa light chains. Non-routine specific immunofluorescence stainings of endomyocardial biopsy specimens were key for the diagnosis of myocardial light chain deposition disease. We discuss non-amyloidotic cardiac immunoglobulin deposition disease in contrast to cardiac amyloidosis. |
