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Document Details :

Title: Hodgkin's disease in a patient with Von Hippel-Lindau disease. A case report.
Author(s): D'HONDT R, THOMAS J, VAN OOSTEROM AT, DEWOLF-PEETERS C
Journal: Acta Clinica Belgica
Volume: 55    Issue: 5   Date: 2000   
Pages: 276-278
DOI: 10.2143/ACB.55.5.1002913

Abstract :






Von Hippel-Lindau (VHL) disease is an autosomal dominant inherited disorder with a predisposition to develop a wide variety of lesions: retinal, cerebellar, spinal and medullar hemangioblastomas, renal cell carcinomas, phaeochromocytomas, and renal, pancreatic and epididymal cysts are the most frequent manifestations of the disease. The prevalence of VHL disease has been estimated to be 1 per 36.000 persons. We report the case of a 68-year-old woman with Von Hippel-Lindau disease who developed high fever with pulmonary and hepatic lesions proven to be Hodgkin’s disease on biopsy. To our knowledge, this is the first report of Hodgkin’s disease in a patient with Von Hippel-Lindau.